11-beta-Hydroxylase Deficiency (CYP11B1) | ![](http://smpdb.ca/super_pathway_visualizations/PW000551/thumb) | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
17-alpha-Hydroxylase Deficiency (CYP17) | ![](http://smpdb.ca/super_pathway_visualizations/PW000542/thumb) | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
17-beta Hydroxysteroid Dehydrogenase III Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000059/thumb) | Disease | NADH / Testosterone / Estrone / Estradiol / Calcium / Androstenedione / Formic acid / Mesoheme / Uridine-5'-Diphosphate / Estrone sulfate / Prasterone sulfate / 5beta-dihydrotestosterone |
2-Aminoadipic 2-Oxoadipic Aciduria | ![](http://smpdb.ca/super_pathway_visualizations/PW000696/thumb) | Disease | Pyridoxal phosphate / Lysine / Glutamic acid / NADH / Flavin adenine dinucleotide / L-Saccharopine |
2-Hydroxyglutric Aciduria (D and L Form) | ![](http://smpdb.ca/super_pathway_visualizations/PW000212/thumb) | Disease | Pyridoxal phosphate / Pyruvic acid / Biotin / Aspartic acid / L-Glutamine / Adenosine phosphate / Succinic acid / Glutamic acid / Glutathione / Glycine / Cysteine / NADH / Alanine / ATP / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Guanosine-5'-Monophosphate / gamma-Aminobutyric acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / Pyrophosphoric acid |
2-Ketoglutarate Dehydrogenase Complex Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000525/thumb) | Disease | Pyruvic acid / Biotin / Succinic acid / NADH / ATP / Magnesium cation / Flavin adenine dinucleotide / Citric acid / Maleic acid |
2-Methyl-3-hydroxybutryl-CoA Dehydrogenase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000061/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
21-Hydroxylase Deficiency (CYP21) | ![](http://smpdb.ca/super_pathway_visualizations/PW000552/thumb) | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
27-Hydroxylase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000697/thumb) | Disease | Glycine / NADH / ATP / Iron / Taurine / Mesoheme / Cholic Acid / Flavin adenine dinucleotide / Palmitic Acid / Pyrophosphoric acid / Taurocholic acid / Cholesterol / Chenodeoxycholic acid / Taurochenodeoxycholic acid |
3-beta-Hydroxysteroid Dehydrogenase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000695/thumb) | Disease | NADH / Progesterone / Hydrocortisone / Mesoheme / Cholesterol / Corticosterone / 20-hydroxycholesterol |
3-Hydroxy-3-methylglutaryl-CoA Lyase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000063/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Hydroxyisobutyric Acid Dehydrogenase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000497/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Hydroxyisobutyric Aciduria | ![](http://smpdb.ca/super_pathway_visualizations/PW000498/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Methylcrotonyl-CoA Carboxylase Deficiency Type I | ![](http://smpdb.ca/super_pathway_visualizations/PW000065/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Methylglutaconic Aciduria Type I | ![](http://smpdb.ca/super_pathway_visualizations/PW000066/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Methylglutaconic Aciduria Type III | ![](http://smpdb.ca/super_pathway_visualizations/PW000067/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Methylglutaconic Aciduria Type IV | ![](http://smpdb.ca/super_pathway_visualizations/PW000214/thumb) | Disease | Pyridoxal phosphate / Biotin / Succinic acid / Glutamic acid / Pyridoxal / Leucine / NADH / Valine / Isoleucine / ATP / Acetoacetic acid / Flavin adenine dinucleotide / alpha-Ketoisocaproic acid / alpha-Ketoisovalerate / Methylmalonic Acid |
3-Methylthiofentanyl Action Pathway | ![](http://smpdb.ca/super_pathway_visualizations/PW000656/thumb) | Drug action | ATP / Norepinephrine / Dopamine / Potassium cation / Calcium / 3-Methylthiofentanyl |
3-Phosphoglycerate Dehydrogenase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000698/thumb) | Disease | Pyridoxal phosphate / Tetrahydrofolic acid / Ademetionine / Pyruvic acid / Arginine / Adenosine phosphate / Serine / Methionine / Glutamic acid / Glycine / Creatine / Cysteine / NADH / Alanine / ATP / Aminolevulinic acid / Magnesium cation / Zinc / N,N-dimethylglycine / Glycocyamine / 3-Hydroxypyruvic Acid / Orotidylic acid / Flavin adenine dinucleotide / Pyruvaldehyde / Formaldehyde / 2-Amino-3-Ketobutyric Acid / D-Serine / Pyrophosphoric acid / Glyoxylic acid / Dexfosfoserine / 2-Oxobutanoic Acid |
4-Hydroxybutyric Aciduria/Succinic Semialdehyde Dehydrogenase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000070/thumb) | Disease | Pyridoxal phosphate / Pyruvic acid / Biotin / Aspartic acid / L-Glutamine / Adenosine phosphate / Succinic acid / Glutamic acid / Glutathione / Glycine / Cysteine / NADH / Alanine / ATP / Magnesium cation / Zinc / 5-O-phosphono-alpha-D-ribofuranosyl diphosphate / Guanosine-5'-Monophosphate / gamma-Aminobutyric acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / Pyrophosphoric acid |
5-Oxoprolinase Deficiency | ![](http://smpdb.ca/super_pathway_visualizations/PW000476/thumb) | Disease | Glutamic acid / Glutathione / Glycine / Cysteine / Alanine / ATP / Zinc / Pidolic acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / S-Methyl glutathione |
5-Oxoprolinuria | ![](http://smpdb.ca/super_pathway_visualizations/PW000074/thumb) | Disease | Glutamic acid / Glutathione / Glycine / Cysteine / Alanine / ATP / Zinc / Pidolic acid / Flavin adenine dinucleotide / gamma-Glutamylcysteine / S-Methyl glutathione |
Abacavir Action Pathway | ![](http://smpdb.ca/super_pathway_visualizations/PW000714/thumb) | Drug action | Adenosine phosphate / ATP / Abacavir / Pyrophosphoric acid |
Abciximab Action Pathway | ![](http://smpdb.ca/super_pathway_visualizations/PW000291/thumb) | Drug action | Abciximab |
Acebutolol Action Pathway | ![](http://smpdb.ca/super_pathway_visualizations/PW000364/thumb) | Drug action | ATP / Acebutolol / Potassium cation / Calcium / Magnesium cation |